Dyke-Davidoff-Masson syndrome is characterized by unilateral atrophy of cerebral hemispheres, enlargement of the ipsilateral sulci, ventricles, and cisternal sp. Dyke-Davidoff-Masson syndrome is a rare condition of unknown frequency resulting from brain injury due to a multitude of causes; especially in. Dyke-Davidoff-Masson Syndrome (DDMS) refers to atrophy or hypoplasia of one cerebral hemisphere. (hemiatrophy) which is secondary to brain insult.

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Create a free personal account to make a comment, download free article PDFs, sign up for alerts and more. Sensory loss and psychiatric manifestations like schizophrenia had been reported rarely. Footnotes Source of Support: Case 4 Case 4. Thank you for updating your details. Cerebral hemiatrophy, Dyke—Davidoff—Masson syndrome, hemiparesis. Unable to dgke the form. Get free access to newly published articles Create a personal account or sign in to: There was subtle thickening of the left hemicranium noted, measuring 4.

Complex partial seizure with secondary generalization also had been reported. Synonyms or Alternate Spellings: Schweizer Archiv fur Neurologie und Psychiatrie.

Our website uses cookies to enhance your experience. Create a free personal account to download free article PDFs, sign up for alerts, and more. MR of maxson hemiatrophy. CT of the brain revealed characteristic features diagnostic of infantile type of cerebral hemiatrophy or Dyke-Davidoff-Masson syndrome. Sign in to make a comment Sign in to your personal account.


Dyke-Davidoff-Masson syndrome

There is also thickening of the calvarium on the left side. The radiological discoveries of the same incorporate cerebral hemiatrophy with homolateral hypertrophy of the skull and sinuses. Author information Copyright and License information Disclaimer. Journal List J Pediatr Neurosci v. It has been reported that DDMS is caused by cerebral insult that may occur in davidofff when the maturation of calvarium has not been completed, or during early life due to brain damage usually traumatic.

Seizures can be focal or generalized. He was seizure free for next 3 months but then unfortunately lost for follow-up. There are two types of DDMS — congenital infantile and acquired.

Dyke-Davidoff-Masson Syndrome

Case 3 Case 3. Rasmussen encephalitis does not show calvarial changes, and Sturge—Weber syndrome additionally shows enhancing pial angiomas and cortical calcifications.

Along with drugs, physiotherapy, occupational therapy, and speech therapy play a significant role in long-term management of the child. Ind J Radiol Imag.

There was no history of significant antenatal or perinatal complications. Purchase access Subscribe to the journal. Dyke—Davidoff—Masson syndrome DDMS is described as skull radiographic and pneumatoencephalographic changes in their series of nine patients whose clinical characteristics included hemiparesis, seizures, facial eyke, and mental retardation which was proposed in by Dyke et al.


Computed tomography in cerebral hemiatrophy.

Dyke-Davidoff-Masson syndrome

There is also compensatory thickening of the skull vault. Plain CT head showing atrophy of left cerebral hemisphere with dilated ipsilateral lateral ventricle, widening of sulci and atrophy of gyri on the left side.

Imaging spectrum includes varying degrees of cerebral hemiatrophy of the affected hemishpere with dilatation of the ipsilateral lateral ventricle and ipsilateral sulcal prominence accompanied by homolateral hypertrophy of the skull and sinuses.

Development of the Nervous system. The bilateral carotid pulsations were normal with no bruit. In our case, the findings of left cerebral hemiatrophy with enlarged cortical sulci, microcephaly, and presentation at the age of 14 months reflect an onset of brain insult after the completion of sulci formation, probably of vascular origin involving left middle cerebral artery. InDyke, Davidoff and Masson first described the syndrome in plain radiographic and pneumoencephalographic changes in a series of nine patients.

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