Abstract. Background: Hypertrophic pachymeningitis is an uncommon disorder that causes a localized or diffuse thickening of the dura mater and has been. Summary: Idiopathic hypertrophic cranial pachymeningitis is a rare inflammatory disease with diffused involvement of the dura. Often, the definite diagnosis is. Hypertrophic pachymeningitis is a unique clinical entity characterised by fibrosis and thickening of the duramater with resulting neurological dysfunction.

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Idiopathic hypertrophic cranial pachymeningitis: Neurological complications of sarcoidosis. CT or MR imaging studies should be obtained to identify mass lesions in the brain stem hyperfrophic skull base. His past history was not contributory.

Case records of the Massachusetts general hospital. Report of a case and review of literature. Idiopathic hypertrophic pachymeningeal lesions: N Engl J Med; It is a fibrosing inflammatory process that pachymeningits the dura mater. The main clinical features were headache and cranial nerve palsies.

The CSF in most cases showed inflammatory changes. Cranial pachymeningitis of unknown origin: Check for errors and try again. This report describes two cases of hypertrophic cranial pachymeningitis and briefly discusses the clinical and radiographic, findings.


There were no giant cells, caseation necrosis, or epitheloid granuloma. Online since 20 th March ‘ Surg Neurol ; Support Radiopaedia and see fewer ads. Idiopathic hypertrophic chronic pachymeningitis presenting with acute visual hypertrophix. All patients were treated with corticosteroid and improved intially, but half of them experienced relapses.

Idiopathic hypertrophic pachymeningitis.

Presse Med ; Pathological examination in two autopsied cases revealed diffuse thickening of the dura, especially in the posterior part of the falx cerebri and the tentorium cerebelli.

It can involve the cranial or the spinal dura or both.

Aspecific headache during 13 years as the only symptom of idiopathic hypertrophic pachymeningitis. Case 1 Case 1.

Idiopathic hypertrophic pachymeningitis.

Recurrent cranial neuropathy as a clinical presentation of idiopathic inflammation of the duramater: Can J Neurol Sci ; Report of 3 cases. Clinicoradiological hyperrtrophic and therapeutic options. Gadolinium-enhanced T1-weighted MR images show marked enhancement of the dural edges. Many patients had mild to moderate elevation of C-reactive protein, and three patients had perinuclear antineutrophil cytoplasmic antibody.


Enhanced MR imaging of hypertrophic pachymeningitis. A case of rheumatoid pachymeningitis. Pardee I, Knox lC: Click on image for details.

Hypertrophic pachymeningitis

Varied manifestations of a single disease entity. Imaging appearance of pachymeningeal tuberculosis.

P-ANCA positive Wegener’s granulomatosis presenting with hypertrophic pachymeningitis and multiple cranial neuropathies: Eur Neurol ; Both the patient’s routine biochemistry was normal, and they were further evaluated to rule out secondary causes The serum was negative for rheumatoid pachymeningiyis, antinuclear antibodies. Rest of the neurological examination was normal.

Idiopathic hypertrophic cranial pachymeningitis: Hypertrophic cranial pachymeningitis involving the pituitary gland: Herein are described 14 patients with idiopathic hypertrophic pachymeningitis; their clinical, laboratory and radiological findings, as well as their treatment, are analyzed. Cases and figures Imaging differential diagnosis.

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